Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000632371 | SCV000753549 | pathogenic | Neurofibromatosis, type 1 | 2024-03-16 | criteria provided, single submitter | clinical testing | This sequence change falls in intron 33 of the NF1 gene. It does not directly change the encoded amino acid sequence of the NF1 protein. RNA analysis indicates that this variant induces altered splicing and may result in an absent or disrupted protein product. This variant is not present in population databases (gnomAD no frequency). This variant has been observed in individual(s) with clinical features of neurofibromatosis type 1 (PMID: 32126153; Invitae). ClinVar contains an entry for this variant (Variation ID: 527490). Studies have shown that this variant results in use of a novel splice site and introduces a premature termination codon (PMID: 32126153). The resulting mRNA is expected to undergo nonsense-mediated decay. For these reasons, this variant has been classified as Pathogenic. |
UAB Medical Genomics Laboratory, |
RCV000632371 | SCV001167428 | pathogenic | Neurofibromatosis, type 1 | 2020-01-20 | criteria provided, single submitter | clinical testing | |
Gene |
RCV003159144 | SCV003853200 | pathogenic | not provided | 2024-09-05 | criteria provided, single submitter | clinical testing | Non-canonical splice site variant demonstrated to result in loss of function (PMID: 32126153); Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 32126153) |