Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000413606 | SCV000491870 | pathogenic | not provided | 2022-10-27 | criteria provided, single submitter | clinical testing | Canonical splice site variant predicted to result in a null allele in a gene for which loss of function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); Also known as c.4836-1G>A; This variant is associated with the following publications: (PMID: 33953802, 27074763) |
Center for Human Genetics, |
RCV000497194 | SCV000782036 | likely pathogenic | Neurofibromatosis, type 1 | 2016-11-01 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV000497194 | SCV002560092 | pathogenic | Neurofibromatosis, type 1 | 2022-03-15 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000497194 | SCV003442715 | pathogenic | Neurofibromatosis, type 1 | 2022-11-25 | criteria provided, single submitter | clinical testing | This sequence change affects an acceptor splice site in intron 35 of the NF1 gene. It is expected to disrupt RNA splicing. Variants that disrupt the donor or acceptor splice site typically lead to a loss of protein function (PMID: 16199547), and loss-of-function variants in NF1 are known to be pathogenic (PMID: 10712197, 23913538). For these reasons, this variant has been classified as Pathogenic. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. ClinVar contains an entry for this variant (Variation ID: 373285). Disruption of this splice site has been observed in individuals with neurofibromatosis type 1 (PMID: 27074763; Invitae). This variant is not present in population databases (gnomAD no frequency). |
Revvity Omics, |
RCV000413606 | SCV003816961 | likely pathogenic | not provided | 2023-01-30 | criteria provided, single submitter | clinical testing | |
Medical Genetics, |
RCV000497194 | SCV000588791 | likely pathogenic | Neurofibromatosis, type 1 | 2017-02-02 | no assertion criteria provided | clinical testing |