Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002314853 | SCV000663256 | likely benign | Hereditary cancer-predisposing syndrome; Cardiovascular phenotype | 2017-05-24 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV000781658 | SCV000919873 | uncertain significance | not specified | 2017-09-19 | criteria provided, single submitter | clinical testing | Variant summary: The NF1 c.6915T>C (p.Asp2305Asp) variant involves the alteration of a non-conserved nucleotide, resulting in a synonymous change. One in silico tool predicts a damaging outcome for this variant. 5/5 splice prediction tools predict no significant impact on normal splicing. ESE finder predicts that this variant may affect ESE site of SF2/ASF. However, these predictions have yet to be confirmed by functional studies. This variant is absent in 246250 control chromosomes. In addition, one clinical diagnostic laboratory classified this variant as uncertain significance. The variant of interest has not, to our knowledge, been reported in affected individuals via publications and/or reputable databases; nor evaluated for functional impact by in vivo/vitro studies. Taken together, this variant is classified as VUS-possibly benign. |
Labcorp Genetics |
RCV000497184 | SCV001629596 | likely benign | Neurofibromatosis, type 1 | 2023-05-30 | criteria provided, single submitter | clinical testing | |
Medical Genetics, |
RCV000497184 | SCV000588828 | uncertain significance | Neurofibromatosis, type 1 | 2017-02-02 | no assertion criteria provided | clinical testing |