Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001056232 | SCV001220664 | pathogenic | Neurofibromatosis, type 1 | 2019-11-19 | criteria provided, single submitter | clinical testing | This variant has been observed in individual(s) with clinical features of neurofibromatosis type 1 (PMID: 7655472). This variant is also known as 7260delT in the literature. For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in NF1 are known to be pathogenic (PMID: 10712197, 23913538). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Leu2421Tyrfs*14) in the NF1 gene. It is expected to result in an absent or disrupted protein product. |