Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
CGC Genetics, |
RCV004765449 | SCV005374868 | likely pathogenic | Neurofibromatosis, type 1 | 2024-04-03 | no assertion criteria provided | clinical testing | The variant NM_000267.3:c.7523del p.(Pro2508Leufs*19), detected in heterozygosity, has not been described in the literature, nor is it reported in the gnomAD database at the time of this submission. It is a frameshift variant that introduces a premature stop codon, which in turn is predicted to lead to the creation of a truncated protein and/or a reduction in its expression due to mRNA degradation. With the information currently available, this should be classified as a probably pathogenic variant. ACMG codes: PVS1; PM2_supporting. |