Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Kasturba Medical College, |
RCV004597213 | SCV005085881 | likely pathogenic | Neurofibromatosis, type 1 | criteria provided, single submitter | clinical testing | The variant likely introduces a prematuretermination codon, which may either result in truncated protein or trigger nonsense-medicated decay.Mono-allelic loss of function variants (nonsense/frameshift) including those located towards the 3’end of NF1 are known to be causative of neurofibromatosis type 1 (Pros E et al.,2008). Thus, above-mentioned findings confirm the diagnosis of neurofibromatosis, type 1. |