Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000572639 | SCV000663113 | uncertain significance | Hereditary cancer-predisposing syndrome | 2016-03-10 | criteria provided, single submitter | clinical testing | The p.P2717L variant (also known as c.8150C>T), located in coding exon 56 of the NF1 gene, results from a C to T substitution at nucleotide position 8150. The proline at codon 2717 is replaced by leucine, an amino acid with similar properties. This variant was not reported in population based cohorts in the following databases: Database of Single Nucleotide Polymorphisms (dbSNP), NHLBI Exome Sequencing Project (ESP), and 1000 Genomes Project. In the ESP, this variant was not observed in 6503 samples (13006 alleles) with coverage at this position.To date, this alteration has been detected with an allele frequency of approximately 0.001% (greater than 110000alleles tested) in our clinical cohort. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive.Since supporting evidence is limited at this time, the clinical significance of this alterationremains unclear. |
Gene |
RCV000681184 | SCV000808642 | uncertain significance | not provided | 2023-03-08 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Observed de novo in an individual undergoing whole exome sequencing due to an orofacial cleft; however, further clinical details were not provided (Bishop et al., 2020); Not observed in any cases, but was observed in unaffected controls from a breast cancer study (Dorling et al., 2021); This variant is associated with the following publications: (PMID: 30089490, 32372504, 25486365, 32574564, 33471991) |
Labcorp Genetics |
RCV000804420 | SCV000944331 | likely benign | Neurofibromatosis, type 1 | 2025-01-23 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV000804420 | SCV002561177 | uncertain significance | Neurofibromatosis, type 1 | 2022-03-15 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002420548 | SCV002678501 | likely benign | Hereditary cancer-predisposing syndrome; Cardiovascular phenotype | 2021-06-22 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Fulgent Genetics, |
RCV002476216 | SCV002781397 | uncertain significance | Neurofibromatosis, familial spinal; Juvenile myelomonocytic leukemia; Neurofibromatosis, type 1; Neurofibromatosis-Noonan syndrome; Café-au-lait macules with pulmonary stenosis | 2021-12-14 | criteria provided, single submitter | clinical testing |