Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000800358 | SCV000940068 | uncertain significance | Neurofibromatosis, type 1 | 2021-03-09 | criteria provided, single submitter | clinical testing | In summary, this variant is a novel missense change with uncertain impact on protein function. It has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0"). This variant is not present in population databases (ExAC no frequency) and has not been reported in the literature in individuals with an NF1-related disease. This sequence change replaces cysteine with arginine at codon 2787 of the NF1 protein (p.Cys2787Arg). The cysteine residue is weakly conserved and there is a large physicochemical difference between cysteine and arginine. |
Baylor Genetics | RCV003461122 | SCV004198278 | uncertain significance | Juvenile myelomonocytic leukemia | 2023-10-03 | criteria provided, single submitter | clinical testing |