Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000820261 | SCV000960967 | pathogenic | Neurofibromatosis, type 1 | 2018-12-22 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in NF1 are known to be pathogenic (PMID: 10712197, 23913538). This variant has been observed in an individual affected with neurofibromatosis type I (PMID: 24789688). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Cys324*) in the NF1 gene. It is expected to result in an absent or disrupted protein product. |
Gene |
RCV002286790 | SCV002577026 | likely pathogenic | not provided | 2022-03-29 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Published functional studies support that this variant results in aberrant splicing (Xu 2014); Not observed at significant frequency in large population cohorts (gnomAD); Identified in a patient with clinically definite or suspected NF1 in published literature (Xu 2014); This variant is associated with the following publications: (PMID: 24789688, Zhang2018[Poster]) |