Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV003134116 | SCV003812788 | uncertain significance | Cutis laxa with severe pulmonary, gastrointestinal and urinary anomalies | 2019-09-06 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004636710 | SCV005130023 | uncertain significance | Inborn genetic diseases | 2024-05-20 | criteria provided, single submitter | clinical testing | The c.727T>C (p.Y243H) alteration is located in exon 6 (coding exon 6) of the LTBP4 gene. This alteration results from a T to C substitution at nucleotide position 727, causing the tyrosine (Y) at amino acid position 243 to be replaced by a histidine (H). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |