Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Undiagnosed Diseases Network, |
RCV004545833 | SCV002098348 | uncertain significance | STAG2-related disorder | 2022-01-06 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002545215 | SCV003031378 | uncertain significance | not provided | 2022-11-08 | criteria provided, single submitter | clinical testing | This variant is present in population databases (rs777893472, gnomAD 0.005%). This sequence change replaces serine, which is neutral and polar, with leucine, which is neutral and non-polar, at codon 97 of the STAG2 protein (p.Ser97Leu). This variant has not been reported in the literature in individuals affected with STAG2-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0"). ClinVar contains an entry for this variant (Variation ID: 1342142). |