Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001993335 | SCV002234447 | pathogenic | Joubert syndrome 14 | 2021-08-04 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Arg59*) in the TMEM237 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in TMEM237 are known to be pathogenic (PMID: 22152675). This variant is not present in population databases (ExAC no frequency). This variant has not been reported in the literature in individuals affected with TMEM237-related conditions. For these reasons, this variant has been classified as Pathogenic. |
Fulgent Genetics, |
RCV001993335 | SCV005654486 | likely pathogenic | Joubert syndrome 14 | 2024-04-23 | criteria provided, single submitter | clinical testing |