Total submissions: 8
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000166650 | SCV000217455 | likely benign | Hereditary cancer-predisposing syndrome | 2014-11-05 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Labcorp Genetics |
RCV000233690 | SCV000285965 | likely benign | Familial adenomatous polyposis 2 | 2024-01-10 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV000166650 | SCV000685670 | likely benign | Hereditary cancer-predisposing syndrome | 2017-01-12 | criteria provided, single submitter | clinical testing | |
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV001284022 | SCV001469579 | likely benign | not provided | 2021-06-29 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001284022 | SCV001848095 | benign | not provided | 2015-03-03 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV000166650 | SCV002532330 | likely benign | Hereditary cancer-predisposing syndrome | 2021-07-11 | criteria provided, single submitter | curation | |
All of Us Research Program, |
RCV000233690 | SCV004835682 | likely benign | Familial adenomatous polyposis 2 | 2023-11-30 | criteria provided, single submitter | clinical testing | |
Department of Pathology and Laboratory Medicine, |
RCV000233690 | SCV001548594 | likely benign | Familial adenomatous polyposis 2 | no assertion criteria provided | clinical testing | The MUTYH p.His26= variant was not identified in the literature nor was it identified in the GeneInsight-COGR, Cosmic, or UMD-LSDB, databases. The variant was identified in dbSNP (ID: rs776396492) as "With Likely benign allele ", and in ClinVar (classified as likely benign by Ambry Genetics, Invitae, Color Genomics). The variant was identified in control databases in 2 of 246264 chromosomes at a frequency of 0.000008 (Genome Aggregation Database Feb 27, 2017). The variant was observed in East Asian population in 2 of 17248 chromosomes (freq: 0.000116), while the variant was not observed in the African, Other, Latino, European, Ashkenazi Jewish, Finnish, and South Asian populations. The p.His26= variant is not expected to have clinical significance because it does not result in a change of amino acid and is not located in a known consensus splice site. In addition, in silico or computational prediction software programs (SpliceSiteFinder, MaxEntScan, NNSPLICE, GeneSplicer, HumanSpliceFinder) do not predict a difference in splicing. In summary, based on the above information the clinical significance of this variant cannot be determined with certainty at this time although we would lean towards a more benign role for this variant. This variant is classified as likely benign. |