Total submissions: 9
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000410208 | SCV000487338 | uncertain significance | Familial adenomatous polyposis 2 | 2016-03-03 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000410208 | SCV000545791 | uncertain significance | Familial adenomatous polyposis 2 | 2024-01-27 | criteria provided, single submitter | clinical testing | This sequence change replaces asparagine, which is neutral and polar, with threonine, which is neutral and polar, at codon 279 of the MUTYH protein (p.Asn279Thr). This variant is present in population databases (rs587778534, gnomAD 0.03%). This missense change has been observed in individual(s) with MUTYH-associated polyposis (Invitae). In at least one individual the data is consistent with being in trans (on the opposite chromosome) from a pathogenic variant. ClinVar contains an entry for this variant (Variation ID: 134857). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be disruptive. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV000491219 | SCV000580082 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-03-27 | criteria provided, single submitter | clinical testing | The p.N279T variant (also known as c.836A>C), located in coding exon 10 of the MUTYH gene, results from an A to C substitution at nucleotide position 836. The asparagine at codon 279 is replaced by threonine, an amino acid with similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV000985864 | SCV001134487 | uncertain significance | not provided | 2021-07-21 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV000491219 | SCV001352103 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-03-08 | criteria provided, single submitter | clinical testing | This missense variant replaces asparagine with threonine at codon 279 of the MUTYH protein. Computational prediction suggests that this variant may have deleterious impact on protein structure and function (internally defined REVEL score threshold >= 0.7, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with MUTYH-related disorders in the literature. This variant has been identified in 3/31360 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Gene |
RCV000985864 | SCV001825652 | uncertain significance | not provided | 2020-02-25 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 24728327) |
All of Us Research Program, |
RCV000410208 | SCV004843250 | uncertain significance | Familial adenomatous polyposis 2 | 2023-03-23 | criteria provided, single submitter | clinical testing | This missense variant replaces asparagine with threonine at codon 279 of the MUTYH protein. Computational prediction tools and conservation analyses suggest that this variant may have deleterious impact on protein structure and function. Splice site prediction tools suggest that this variant may not impact RNA splicing. To our knowledge, functional studies have not been performed for this variant. This variant has not been reported in individuals affected with hereditary cancer in the literature. This variant has been identified in 3/31360 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Baylor Genetics | RCV000410208 | SCV005056029 | uncertain significance | Familial adenomatous polyposis 2 | 2024-03-19 | criteria provided, single submitter | clinical testing | |
ITMI | RCV000121590 | SCV000085786 | not provided | not specified | 2013-09-19 | no assertion provided | reference population |