Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001058037 | SCV001222573 | uncertain significance | Epilepsy, familial focal, with variable foci 3 | 2023-08-27 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This sequence change replaces glutamic acid, which is acidic and polar, with lysine, which is basic and polar, at codon 557 of the NPRL3 protein (p.Glu557Lys). This variant is present in population databases (rs764005661, gnomAD 0.02%). This variant has not been reported in the literature in individuals affected with NPRL3-related conditions. ClinVar contains an entry for this variant (Variation ID: 853258). Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. |