Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Kasturba Medical College, |
RCV001806382 | SCV002053940 | likely pathogenic | Muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A, 4 | criteria provided, single submitter | research | ||
Neuberg Centre For Genomic Medicine, |
RCV003339749 | SCV004047143 | uncertain significance | Autosomal recessive limb-girdle muscular dystrophy type 2M | criteria provided, single submitter | clinical testing | The splice region variant c.165+5G>A in FKTN (NM_001079802.2) has been reported to ClinVar as Likely Pathogenic but no details are available for independent assessment. The c.165+5G>A variant is novel (not in any individuals) in gnomAD Exomes and is novel (not in any individuals) in 1000 Genomes. The nucleotide c.165+5G>A in FKTN is predicted conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance (VUS). |