Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000671524 | SCV000796508 | likely pathogenic | Muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A, 4 | 2017-12-27 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000800445 | SCV000940160 | pathogenic | Walker-Warburg congenital muscular dystrophy | 2018-11-06 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (ExAC no frequency). For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in FKTN are known to be pathogenic (PMID: 17044012, 17878207, 18752264). This variant has been observed in an individual affected with muscular dystrophy (PMID: 19396839). ClinVar contains an entry for this variant (Variation ID: 555661). This sequence change creates a premature translational stop signal (p.Leu15*) in the FKTN gene. It is expected to result in an absent or disrupted protein product. |
OMIM | RCV002282313 | SCV000023530 | pathogenic | Muscular dystrophy-dystroglycanopathy (congenital without intellectual disability), type B4 | 2009-05-26 | no assertion criteria provided | literature only |