Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000518924 | SCV000618881 | uncertain significance | not provided | 2017-07-07 | criteria provided, single submitter | clinical testing | A variant of uncertain significance has been identified in the FKTN gene. The c.82_84delTAC variant has not been published as a pathogenic variant, nor has it been reported as a benign variant to our knowledge. The c.82_84delTAC variant is not observed in large population cohorts (Lek et al., 2016). The c.82_84delTAC variant results in an in-frame deletion of a single tyrosine (Y) residue, denoted p.Y28del. This variant occurs at a position that is conserved in mammals. However, in-frame deletions and duplications have not been reported at nearby residues in the Human Gene Mutation Database in association with FKTN-related disorders (Stenson et al., 2014). |