Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004185750 | SCV003680844 | uncertain significance | not specified | 2022-08-16 | criteria provided, single submitter | clinical testing | The c.86C>T (p.T29M) alteration is located in exon 1 (coding exon 1) of the SLC45A1 gene. This alteration results from a C to T substitution at nucleotide position 86, causing the threonine (T) at amino acid position 29 to be replaced by a methionine (M). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Neuberg Centre For Genomic Medicine, |
RCV004577032 | SCV005061210 | uncertain significance | Intellectual developmental disorder with neuropsychiatric features | 2023-06-22 | criteria provided, single submitter | clinical testing | The missense c.86C>T (p.Thr29Met) variant in the SLC45A1 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is reported with the allele frequency of 0.01% in the gnomAD Exomes. This variant has been reported to the ClinVar database as Uncertain significance. Computational evidence (SIFT - Damaging and MutationTaster -Disease causing) predicts conflicting evidence on protein structure and function for this variant. The reference amino acid at this position in SLC45A1 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. The amino acid Threonine at position 29 is changed to a Methionine changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as Variant of Uncertain Significance (VUS). |