Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002513314 | SCV003443444 | pathogenic | not provided | 2023-12-17 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Arg312*) in the CCDC88C gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in CCDC88C are known to be pathogenic (PMID: 23042809, 29225145). This variant is present in population databases (rs369384363, gnomAD 0.04%). This premature translational stop signal has been observed in individual(s) with congenital hydrocephalus (PMID: 23042809). It has also been observed to segregate with disease in related individuals. ClinVar contains an entry for this variant (Variation ID: 39861). For these reasons, this variant has been classified as Pathogenic. |
Fulgent Genetics, |
RCV005007923 | SCV005637719 | pathogenic | Hydrocephalus, nonsyndromic, autosomal recessive 1; Spinocerebellar ataxia type 40 | 2024-01-22 | criteria provided, single submitter | clinical testing | |
OMIM | RCV000033088 | SCV000056868 | pathogenic | Hydrocephalus, nonsyndromic, autosomal recessive 1 | 2018-07-10 | no assertion criteria provided | literature only |