Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004726764 | SCV005334408 | likely pathogenic | not provided | 2023-08-27 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: Muthusamy2022[casereport], 34976470, 32116545) |
Sydney Children's Hospital, |
RCV000991320 | SCV001132792 | uncertain significance | X-linked intellectual disability-short stature-overweight syndrome | 2019-01-10 | no assertion criteria provided | clinical testing |