Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001837659 | SCV002098237 | uncertain significance | not provided | 2022-02-18 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
OMIM | RCV003487010 | SCV004242168 | pathogenic | Leukoencephalopathy-thalamus and brainstem anomalies-high lactate syndrome | 2024-01-26 | no assertion criteria provided | literature only |