Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001009224 | SCV001169043 | likely pathogenic | not provided | 2021-01-11 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation or nonsense-mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed in large population cohorts (Lek et al., 2016); Has not been previously published as pathogenic or benign to our knowledge |
Illumina Laboratory Services, |
RCV003985097 | SCV004801448 | likely pathogenic | Microcephaly 2, primary, autosomal recessive, with or without cortical malformations | 2021-08-06 | criteria provided, single submitter | clinical testing | The WDR62 c.4234dupC p.(Leu1412ProfsTer2) variant causes a shift in the protein reading frame that is predicted to result in premature termination of the protein. Loss of normal protein function through either protein truncation or nonsense-mediated mRNA decay is expected. To our knowledge, this variant has not been reported in the peer-reviewed literature. Variants downstream of the p.(Leu1412ProfsTer2) variant have also been reported (Landrum et al. 2016; Zombor et al. 2019). This variant is reported in the Genome Aggregation Database in one allele at a frequency of 0.000024 in the African/African-American population (version 3.1.2). Based on the available evidence the c.4234dupC p.(Leu1412ProfsTer2) variant is classified as likely pathogenic for microcephaly with or without cortical malformations. |