Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV000191133 | SCV000245542 | pathogenic | Pitt-Hopkins syndrome | 2014-07-10 | criteria provided, single submitter | clinical testing | This splice site variant is categorized as deleterious according to ACMG guidelines (PMID:18414213) and was found once in our laboratory de novo in a 21-year-old female with severe intellectual disability, seizure disorder, ataxia, self-stimulatory behavior, dysmorphisms, short stature, macrocephaly, obesity |