Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV000560032 | SCV005200078 | likely benign | Pitt-Hopkins syndrome | 2024-06-25 | reviewed by expert panel | curation | The p.Ser102Asn variant in TCF4 is present in 1 XX individual in gnomAD v4.0 (0.00016%) (not sufficient to meet BS1 criteria). The p.Ser102Asn variant is observed in at least 2 unaffected individuals (internal database - GeneDx) (BS2). Computational analysis prediction tools suggest that the p.Ser102Asn variant does not have a deleterious impact; however this information does not predict clinical significance on its own (BP4). In summary, the p.Ser102Asn variant in TCF4 is classified as likely benign based on the ACMG/AMP criteria (BS2, BP4). |
Gene |
RCV000189717 | SCV000243365 | likely benign | not provided | 2022-08-05 | criteria provided, single submitter | clinical testing | See Variant Classification Assertion Criteria. |
Labcorp Genetics |
RCV000560032 | SCV000646127 | uncertain significance | Pitt-Hopkins syndrome | 2021-09-01 | criteria provided, single submitter | clinical testing |