Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002857955 | SCV003228707 | pathogenic | not provided | 2022-11-08 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has not been reported in the literature in individuals affected with MYSM1-related conditions. This sequence change creates a premature translational stop signal (p.Asp92Glufs*2) in the MYSM1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in MYSM1 are known to be pathogenic (PMID: 24288411, 28115216). This variant is present in population databases (rs755178846, gnomAD 0.0009%). |