Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV001841018 | SCV001354785 | likely benign | Cardiac arrhythmia | 2019-01-07 | criteria provided, single submitter | clinical testing | |
Petrovsky National Research Centre of Surgery, |
RCV001293777 | SCV001482442 | benign | Congenital long QT syndrome | 2021-03-03 | criteria provided, single submitter | clinical testing | We observed a genetic variant g.38655522G>A (NM_001160161.1: c.647C>T, p.S216L) in a female proband of 14 y.o. with QT interval prolongation on ECG. This variant was also found in proband’s mother with normal ECG. This variant was evaluated according to ACMG criteria. BS1: Allele frequency is greater than expected for disorder; BS4: Lack of segregation in affected members of a family. Furthermore, noncanonical transcripts of exon 6 of the SCN5A gene containing this variant are poorly represented in cardiac tissue (gnomAD). Based on this evidences the g.38655522G>A (NM_001160161.1: c.647C>T, p.S216L variant is classified as Benign. |