Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004719637 | SCV005326079 | likely pathogenic | not provided | 2023-10-25 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging effect on protein function (PMID: 19185524); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 26085218, 26240016, 19414794, 24682681, 18350553, 28679735, 15661019, 26230867, 22236433, 36569938, 25703555, 16818673, 25764117, 27744027, 24840983, 31123910, 35289316, 35159348, 18851874, 19185524) |
OMIM | RCV000012222 | SCV000032456 | pathogenic | Immunodeficiency 33 | 2006-07-10 | no assertion criteria provided | literature only |