Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001998489 | SCV002262790 | uncertain significance | Developmental and epileptic encephalopathy, 36 | 2022-07-06 | criteria provided, single submitter | clinical testing | Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. ClinVar contains an entry for this variant (Variation ID: 1477970). This variant has not been reported in the literature in individuals affected with ALG13-related conditions. This variant is present in population databases (rs750251838, gnomAD 0.02%), including at least one homozygous and/or hemizygous individual. This variant, c.476_481del, results in the deletion of 2 amino acid(s) of the ALG13 protein (p.Gly159_Leu160del), but otherwise preserves the integrity of the reading frame. |