Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001753412 | SCV001985473 | uncertain significance | not provided | 2020-09-16 | criteria provided, single submitter | clinical testing | Has been reported in a male patient with sporadic periventricular heterotopia in published literature (Sheen et al., 2001); Not observed at a significant frequency in large population cohorts (Lek et al., 2016); In silico analysis supports that this missense variant does not alter protein structure/function; This variant is associated with the following publications: (PMID: 11532987, 22366253) |
Labcorp Genetics |
RCV001857335 | SCV002129292 | benign | Heterotopia, periventricular, X-linked dominant; Melnick-Needles syndrome; Oto-palato-digital syndrome, type II; Frontometaphyseal dysplasia | 2024-06-21 | criteria provided, single submitter | clinical testing | |
Centre de Biologie Pathologie Génétique, |
RCV002273924 | SCV002559095 | likely pathogenic | Neurodevelopmental delay | criteria provided, single submitter | clinical testing | ||
OMIM | RCV000012518 | SCV000032752 | pathogenic | Heterotopia, periventricular, X-linked dominant | 2001-08-15 | no assertion criteria provided | literature only |