Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clin |
RCV004797644 | SCV005419054 | likely benign | Rett syndrome | 2024-10-30 | reviewed by expert panel | curation | The p.Asp23Glu variant in MECP2 (NM_004992.4) is observed in at least 2 unaffected individuals (internal database - Invitae) (BS2). The highest population minor allele frequency of the p.Asp23Glu variant in MECP2 in gnomAD v4.1 is 0.00006532 in the Admixed American population (not sufficient to meet BS1 criteria). In summary, the p.Asp23Glu variant in MECP2 is classified as Likely Benign based on the ACMG/AMP criteria (BS2). |
Gene |
RCV003314837 | SCV004014141 | uncertain significance | not provided | 2023-01-11 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
Labcorp Genetics |
RCV003523156 | SCV004300789 | benign | Severe neonatal-onset encephalopathy with microcephaly | 2023-08-04 | criteria provided, single submitter | clinical testing |