Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000801736 | SCV000941529 | uncertain significance | Symmetrical dyschromatosis of extremities; Aicardi-Goutieres syndrome 6 | 2018-09-10 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (ExAC no frequency). This sequence change falls in intron 3 of the ADAR gene. It does not directly change the encoded amino acid sequence of the ADAR protein, but it affects a nucleotide within the consensus splice site of the intron. This variant has not been reported in the literature in individuals with ADAR-related disease. Nucleotide substitutions within the consensus splice site are a relatively common cause of aberrant splicing (PMID: 17576681, 9536098). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |