Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Beijing Key Laboratory for Genetic Research of Skeletal Deformity, |
RCV000656327 | SCV000747772 | pathogenic | Cerebral arteriovenous malformation | 2018-02-14 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002536312 | SCV003459988 | pathogenic | Hereditary hemorrhagic telangiectasia | 2022-10-08 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Asn307Lysfs*27) in the ENG gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in ENG are known to be pathogenic (PMID: 15879500). This variant is not present in population databases (gnomAD no frequency). This premature translational stop signal has been observed in individual(s) with clinical features of ENG-related conditions (PMID: 30120215). ClinVar contains an entry for this variant (Variation ID: 545104). For these reasons, this variant has been classified as Pathogenic. |