Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV001843884 | SCV002103086 | uncertain significance | not provided | 2022-01-24 | criteria provided, single submitter | clinical testing | PM2, PM4 |
Labcorp Genetics |
RCV003611562 | SCV004485124 | uncertain significance | Beckwith-Wiedemann syndrome | 2022-12-24 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (gnomAD no frequency). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. This variant has not been reported in the literature in individuals affected with CDKN1C-related conditions. This variant, c.422_427del, results in the deletion of 2 amino acid(s) of the CDKN1C protein (p.Val141_Pro142del), but otherwise preserves the integrity of the reading frame. |