Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003338903 | SCV004047283 | uncertain significance | Waardenburg syndrome type 4A | criteria provided, single submitter | clinical testing | The missense variant c.688G>C (p.Val230Leu) in EDNRB gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Val230Leu variant is novel (not in any individuals) in gnomAD exomes and 1000 Genomes. The amino acid Val at position 230 is changed to a Leu changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as Uncertain Significance (VUS). |