Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV003994921 | SCV004813553 | pathogenic | Familial hypokalemia-hypomagnesemia | 2024-02-15 | criteria provided, single submitter | clinical testing | Variant summary: SLC12A3 c.2841delC (p.Trp948GlyfsX19) results in a premature termination codon, predicted to cause absence of the protein due to nonsense mediated decay, which is a commonly known mechanism for disease. The variant was absent in 251426 control chromosomes (gnomAD). To our knowledge, no occurrence of c.2841delC in individuals affected with Familial Hypokalemia-Hypomagnesemia and no experimental evidence demonstrating its impact on protein function have been reported. No submitters have cited clinical-significance assessments for this variant to ClinVar. Based on the evidence outlined above, the variant was classified as pathogenic. |