Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Johns Hopkins Genomics, |
RCV001804220 | SCV002051774 | likely pathogenic | Familial hypokalemia-hypomagnesemia | 2021-12-01 | criteria provided, single submitter | clinical testing | SLC12A3 c.2938G>A has been reported in multiple individuals with Gitelman syndrome. Functional studies suggest that this substitution alters SLC12A3 protein localization in cells. This variant (rs34803727) is rare (<0.1%) in a large population dataset (gnomAD: 17/282386 total alleles; 0.006%; no homozygotes) and has been reported in ClinVar (Variation ID: 586605). We consider SLC12A3 c.2938G>A to be likely pathogenic. |