Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV003985594 | SCV004107008 | likely pathogenic | CACNA1A-related disorder | 2023-08-11 | criteria provided, single submitter | clinical testing | The CACNA1A c.5780_5783dupTGGC variant is predicted to result in a frameshift and premature protein termination (p.Ile1929Glyfs*134). To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. Frameshift variants in CACNA1A are expected to be pathogenic. This variant is interpreted as likely pathogenic. |