Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000439656 | SCV000536574 | uncertain significance | not provided | 2017-02-03 | criteria provided, single submitter | clinical testing | The A2258G variant in the CACNA1A gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The A2258G variant was not observed in the Exome Aggregation Consortium (ExAC) data set, indicating it is not a common benign variant. The A2258G variant is a conservative amino acid substitution, which is not likely to impact secondary protein structure as these residues share similar properties. This substitution occurs at a position that is not conserved. In silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. We interpret A2258G as a variant of uncertain significance. |