Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV003985603 | SCV004110243 | uncertain significance | CACNA1A-related disorder | 2023-04-07 | criteria provided, single submitter | clinical testing | The CACNA1A c.6958C>T variant is predicted to result in premature protein termination (p.Gln2320*). To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. Although this variant is predicted to result in an early termination change, it is located in the terminal exon, and other early termination changes are observed nearby in the gnomAD database of individuals with unknown phenotypes. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |