Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001942154 | SCV002236310 | pathogenic | Episodic ataxia type 2; Developmental and epileptic encephalopathy, 42 | 2023-05-22 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (gnomAD no frequency). For these reasons, this variant has been classified as Pathogenic. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is expected to disrupt CACNA1A protein function. ClinVar contains an entry for this variant (Variation ID: 1454996). This missense change has been observed in individual(s) with CACNA1A-related conditions (PMID: 25596066). In at least one individual the variant was observed to be de novo. This sequence change replaces cysteine, which is neutral and slightly polar, with tyrosine, which is neutral and polar, at codon 272 of the CACNA1A protein (p.Cys272Tyr). |
Greenwood Genetic Center Diagnostic Laboratories, |
RCV002291304 | SCV002583725 | likely pathogenic | CACNA1A-related disorder | 2022-09-28 | criteria provided, single submitter | clinical testing | PM6 PM2 PS4_moderate PP2 PP3 |