Total submissions: 10
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000179740 | SCV000232037 | uncertain significance | not provided | 2014-11-15 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000362732 | SCV000415920 | uncertain significance | Renal dysplasia and retinal aplasia | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000270468 | SCV000415921 | uncertain significance | Nephronophthisis | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000309235 | SCV000415922 | uncertain significance | Familial aplasia of the vermis | 2016-06-14 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000270468 | SCV001380742 | uncertain significance | Nephronophthisis | 2024-01-08 | criteria provided, single submitter | clinical testing | This variant, c.644_646dup, results in the insertion of 1 amino acid(s) of the NPHP1 protein (p.Glu215dup), but otherwise preserves the integrity of the reading frame. This variant is present in population databases (rs777677768, gnomAD 0.07%), including at least one homozygous and/or hemizygous individual. This variant has not been reported in the literature in individuals affected with NPHP1-related conditions. ClinVar contains an entry for this variant (Variation ID: 198410). Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Gene |
RCV000179740 | SCV001873683 | uncertain significance | not provided | 2021-08-18 | criteria provided, single submitter | clinical testing | Has not been previously published as pathogenic or benign to our knowledge |
Mayo Clinic Laboratories, |
RCV000179740 | SCV002541850 | uncertain significance | not provided | 2021-12-29 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV002485176 | SCV002784209 | likely benign | Joubert syndrome with renal defect; Nephronophthisis 1; Senior-Loken syndrome 1 | 2024-03-01 | criteria provided, single submitter | clinical testing | |
Breakthrough Genomics, |
RCV000179740 | SCV005187856 | uncertain significance | not provided | criteria provided, single submitter | not provided | ||
Prevention |
RCV004734799 | SCV005346070 | uncertain significance | NPHP1-related disorder | 2024-07-23 | no assertion criteria provided | clinical testing | The NPHP1 c.644_646dupAAG variant is predicted to result in an in-frame duplication (p.Glu215dup). To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.072% of alleles in individuals of Latino descent in gnomAD. Although we suspect this variant may be benign, at this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |