Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001233094 | SCV001405675 | pathogenic | Familial adenomatous polyposis 2 | 2019-07-26 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Pro3Hisfs*41) in the MUTYH gene. It is expected to result in an absent or disrupted protein product. For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in MUTYH are known to be pathogenic (PMID: 18534194, 20663686). This variant has not been reported in the literature in individuals with MUTYH-related conditions. This variant is not present in population databases (ExAC no frequency). |