Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000523828 | SCV000621451 | uncertain significance | not provided | 2017-10-09 | criteria provided, single submitter | clinical testing | The G356S variant in the SLC39A14 gene has not been reported previously as a pathogenic variant, nor as a benign variant, to our knowledge. The G356S variant is not observed at a significant frequency in large population cohorts (Lek et al., 2016). The G356S variant is a non-conservative amino acid substitution, which is likely to impact secondary protein structure as these residues differ in polarity, charge, size and/or other properties. This substitution occurs at a position that is conserved across species. In silico analysis predicts this variant is probably damaging to the proteinstructure/function. We interpret G356S as a variant of uncertain significance. |
OMIM | RCV001814184 | SCV002061330 | pathogenic | Hypermanganesemia with dystonia 2 | 2022-01-19 | no assertion criteria provided | literature only |