Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center of Excellence in Genomics and Precision Dentistry, |
RCV001789734 | SCV002032063 | pathogenic | Brachyolmia-amelogenesis imperfecta syndrome | criteria provided, single submitter | clinical testing | A homozygous splice site mutation, c.1721-2A>G, in splice site acceptor (SSA) region before exon 12 of LTBP3 gene was identified in a patient with dental anomalies and short stature (DASS). Her parents were heterozygous for the mutation (Intarak et. al. 2019). |