Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV002260574 | SCV002540268 | uncertain significance | Developmental and epileptic encephalopathy, 5 | 2022-02-17 | criteria provided, single submitter | clinical testing | The SPTAN1 c.4804G>A (p.Ala1602Thr) missense variant results in the substitution of alanine at position 1602 with threonine. To our knowledge, this variant has not been reported in the peer-reviewed literature. This variant is reported in the Genome Aggregation Database in one allele at a frequency of 0.000009 in the European (non-Finnish) population (version 2.1.1). Based on the available evidence, the c.4804G>A (p.Ala1602Thr) variant is classified as a variant of uncertain significance for SPTAN1-related developmental and epileptic encephalopathy. |