Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000657889 | SCV000779652 | pathogenic | not provided | 2020-07-10 | criteria provided, single submitter | clinical testing | In-frame deletion of 1 amino acid in a non-repeat region; Published functional studies suggest this variant may disrupt normal protein function (Hamdan et al., 2012); In silico analysis supports a deleterious effect on protein structure/function; Not observed in large population cohorts (Lek et al., 2016); This variant is associated with the following publications: (PMID: 22258530, 29337302, 25631096, 33163565) |
OMIM | RCV000029155 | SCV000051800 | pathogenic | Developmental and epileptic encephalopathy, 5 | 2012-07-01 | no assertion criteria provided | literature only |