Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001839094 | SCV002098998 | uncertain significance | Landau-Kleffner syndrome | 2021-02-24 | criteria provided, single submitter | clinical testing | The inherited c.4324C>G, p.Pro1442Ala missense variant identified in GRIN2A has not been reported in the literature. This variant has one heterozygote in the gnomAD v3.1database, indicating this is a rare allele. Iin silico analysis predicts conflicting effect of pathogenicity [PMID:27268795] and the position is strongly conserved (GERP++ = 5.79). Based on the available evidence, the missense variant c.4324C>G, p.Pro1442Ala in the GRIN2A gene is classified as a Variant of Uncertain Significance. |