Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000255072 | SCV000321401 | likely pathogenic | not provided | 2023-06-27 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 25998749, 31046801, 31589614, 37294112, 33435499) |
Baylor Genetics | RCV001289511 | SCV001522023 | pathogenic | Autosomal recessive congenital ichthyosis 2 | 2019-10-04 | criteria provided, single submitter | clinical testing | This variant was determined to be pathogenic according to ACMG Guidelines, 2015 [PMID:25741868]. |
Mendelics | RCV001289511 | SCV002516221 | likely pathogenic | Autosomal recessive congenital ichthyosis 2 | 2022-05-04 | criteria provided, single submitter | clinical testing | |
Ce |
RCV000255072 | SCV005074610 | likely pathogenic | not provided | 2024-06-01 | criteria provided, single submitter | clinical testing | ALOX12B: PM3:Strong, PM2, PM5, PP4 |
Fulgent Genetics, |
RCV001289511 | SCV005652828 | likely pathogenic | Autosomal recessive congenital ichthyosis 2 | 2024-05-09 | criteria provided, single submitter | clinical testing | |
Institute for Human Genetics, |
RCV001289511 | SCV001477384 | pathogenic | Autosomal recessive congenital ichthyosis 2 | 2021-01-07 | no assertion criteria provided | clinical testing |