Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV003460067 | SCV004195230 | likely pathogenic | Retinitis pigmentosa 25 | 2023-07-27 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV003779018 | SCV004655054 | pathogenic | not provided | 2023-03-12 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with EYS-related conditions. For these reasons, this variant has been classified as Pathogenic. Information on the frequency of this variant in the gnomAD database is not available, as this variant may be reported differently in the database. This sequence change creates a premature translational stop signal (p.Cys860*) in the EYS gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in EYS are known to be pathogenic (PMID: 18836446, 20333770). |